Pathophysiology / Overview
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Signs and Symptoms
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Red Flags / Danger Signs
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Nursing Assessment and Interventions
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Clinical Pearls
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Client Education
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Your exam focus
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Next steps
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Overview
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Overview
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Key Concept
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Common Defects With Decreased Pulmonary Blood Flow
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Ventricular septal defect
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Right ventricular hypertrophy
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RN assessment findings
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Cyanosis, especially with crying or feeding
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Hypercyanotic “Tet” Spells
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Triggers
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Crying
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Findings
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Sudden deep cyanosis
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RN interventions
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Place infant in knee-chest position
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Notify provider or rapid response team
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RN assessment findings
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Cyanosis shortly after birth
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Signs of hypoxemia
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RN priorities
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Monitoring oxygen saturation
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Preparing family for staged surgical repair
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Critical concept
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RN priorities
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Prostaglandin E1 infusion to keep the ductus arteriosus open
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Pulse oximetry
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Preparation for cardiac intervention or surgery
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Murmur
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Expected Clinical Manifestations
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Cyanosis
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RN Assessment Priorities
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Respiratory status
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Respiratory rate
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Cardiovascular status
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Heart rate
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Feeding and growth
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Feeding duration
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Neurologic status
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Irritability
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Promote oxygenation
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Administer oxygen as ordered
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Manage tet spells
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Place infant in knee-chest position
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Support feeding
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Small, frequent feeds
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Rest periods during feeding
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Daily weights
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Prevent dehydration
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Monitoring intake and output
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Prepare for surgery
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Preoperative teaching
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Prostaglandin E1
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Apnea
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Beta-blockers
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Heart rate
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Morphine
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Respiratory depression
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Parent Teaching
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Increased cyanosis
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Cyanotic spell that does not improve with positioning
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Clinical Judgment Priority
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